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Sindromul Mediastinal -Curs 2013

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    SINDROMUL MEDIASTINAL

    Dr. Anca Mihailescu

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    Cuprins

    Delimitarea mediastinului si acompartimentelor sale

    Semnele si simptomele SM Explorarea functionala si paraclinica a SM

    Patologie mediastinala

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    MEDIASTIN- DELIMITARE

    Inferior diafragm

    Superior apertura toracica superioara

    Lateral

    pleure Anterior stern

    Posterior - coloana vertebrala

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    MEDIASTIN - CONTINUT

    Cord

    Ao, AP, VCS, VCI

    Vase limfatice, ggl

    Trahee, bronhii principale

    Esofag

    Nervii vagi, laringei recurenti, frenici, ic, lanturilesimpatice

    Timus

    Tesut conjunctiv

    Ty, Pty ectopice

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    SINDROM

    SINDROM = semne + simptome careapar adesea impreuna in diferite boli

    cu etiologii diferite- tumorale

    - vasculare

    - infectioase

    - inflamatorii

    - de dezvoltare

    - traumatice

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    Mediastinul superior

    Trahee

    Esofag superior

    Timus

    Arc aortic

    N X N frenici

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    Mediastinul anterosuperior

    Tesut gras

    Ganglioni limfatici

    Tiroida ectopica Timus

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    Mediastinul mijlociu

    Cord

    Aorta ascendenta

    VCS, VCI, vvbrahiocefalice

    Vase pulmonare

    N frenici Ganglioni

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    Mediastinul posterior

    Esofag

    Canal toracic

    Vv azygos,hemiazygos

    Aorta descendenta

    Nn vagi, intercostali

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    SIMPTOME

    Dispnee, tuse, disfonie

    Durere

    Disfagie, sughit, varsatura

    Sincopa

    Cefalee, ameteli, somnolenta, tulburaride vedere

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    DISPNEE

    Compresie extrinseca a traheei

    Obstructie bronsica

    Iritatia n X Pareza de CV stg

    Limitarea miscarilor resp durere

    Pareza de frenic Tamponada pericardica

    Revarsat lichidian pleural

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    TUSEA

    Chintoasa

    Latratoare compresii traheobronsice

    Bitonala pareza laringeu recurent

    Afona distructii de CV

    Surda Hemoptoica staza, T br, ruptura de Ao

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    DISFONIA

    >2-3 sapt semnal

    Sdr Ortner

    - fonastenie

    - afonie

    - raguseala - diplofonie

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    DUREREA TORACICA

    Nespecifica

    Nevralgica frenica

    - ic

    - cervicobrahiala

    Terebranta

    osteita sternala

    Pseudoanginoasa

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    SIMPTOME DIGESTIVE

    Disfagia compresie, obstructie,inflamatie

    Sughit- iritatie frenica

    Varsatura - +vag, afectiuni esofagiene

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    SEMNE MAJORE

    Cianoza

    Edem

    Circulatie colaterala

    Sb mica, Sp mare

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    SEMNE (I, P)

    Anizocorie, sdr Claude Bernard Horner

    Retractii - mediastinita retractila, atelectazie

    Bombari anevrism Ao

    Adenopatii, splenomegalie Puncte Valleix

    Emfizem sc

    Anizosfigmie

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    SEMNE (P, A)

    Matitate interscapulovertebral- sternala superioara

    - rotunjita deasupra cordului- baza toracelui

    - segmentara

    Obstructie localizata/ abolirea MV

    SS parasternal stg

    S Hamman

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    Rg pulmonara (f,p)

    Masa mediastinala vs sdr mediastinal

    Largirea mediastinului

    Rx :Pulsatilitate

    Rata cresterii masei mediastinale

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    CT

    De rutina in SM

    Dg cert de anevrism Ao, lipomatoza

    mediastinala, grasime pericardica Localizare, extindere, invazie, circulatia

    colaterala

    Semne indirecte de malignitate (invazie, meta)

    Ghidaj

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    RMN

    Afectare nervoasa, vasculara

    Leziuni apropiate de apertura

    superioara

    Invazie diafragmatica

    CI la substanta de contrast (alergie, IR)

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    ECO

    Chist vs solid

    Ghidaj biopsie

    Copii

    Leziuni E/periE (ecoendoscopie)

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    ESOFAGOGRAFIA SI EDS

    Afectiuni intrinseci E (diverticuli, cesofagian)

    Compresie extrinseca

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    SCINTIGRAFIE

    I 131, I 123 Tiroida

    Ga 67- limfom

    I-metilbenzilguanina

    feocromocitom

    Selenometionina PTy

    Tc pertechnetat chiste neuroenterice(mucoasa gastrica)

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    INVESTIGATII INVAZIVE

    Bronhoscopie spalare (BAL), periaj, biopsie

    Toracotomie

    VATS biopsie pleurala/ pulmonara

    Mediastinoscopie (suprasternal) nu Ap Ao-pulm, paratraheali stg

    Mediastinotomie parasternal

    Biopsia medulara Biopsia excizionala

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    MANIFESTARI ASOCIATE

    Hipoglicemie mezoteliom, teratom,fibrosarcom

    Sdr Cushing

    Hipercalcemie T Pty

    Simptome neurologice T neurogene

    Miastenia gravis - timom

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    EPIDEMIOLOGIE

    Adulti frecvent AS

    Copii frecvent P

    Simptome ~ malignitate

    Leziuni maligne mai frecvente la copii

    Lf in crestere

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    PATOLOGIE MEDIASTINALA

    Acuta/ cronica

    Tumorala/netumorala (hernii, chiste,infectioasa, inflamatorie, traumatica)

    M superior/anterior/ mijlociu/ posterior

    /difuz

    Frecventa/rara

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    AFECTIUNI MEDIASTINALE

    frecvente rare

    Anterosuperior TimomLimfomT germinale

    Leziuni vasculareT mezenchimale

    T endocrine

    Mijlociu Chiste bronhogeneT limfoide

    Chiste pericardice

    Chiste gastro

    Posterior T neurogene Leziuni vasculareT mezenchimale

    Leziuni limfoide

    Hernie Bochdalek

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    PNEUMOMEDIASTIN

    Durere in inspir, dispnee, disfonie

    Crepitatii sc

    Context clinic

    posttraumatic/ barotrauma/ruptura esofagiana

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    MEDIASTINITA ACUTA

    Perforatie esofagiana Sdr. Boerhaave

    - prognostic prost

    - durere brusca, febra- Rx - pneumomediastin, hidroptx- tranzit baritat- TCTrat: chirurgical+Ab

    Post sternotomie (in I sapt, < 1%, Mo 15%) Perforatia traheobronsica Prin contiguitate

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    Esofagograma cu gastrografin Sdr.Boerhaave

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    MEDIASTINITA CRONICA SIFIBROZA MEDIASTINALA

    Sdr de VCS

    Peric constrictiva

    Obstructie de AP Obstructie

    traheobronsica

    Evolutie lenta

    CT, Rx, angiografie

    Culturi -

    Histoplasmoza

    Mycobacterii

    Candida Iradiere

    Metisergida

    B autoimune

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    PATOLOGIE TUMORALA

    Ap metastatice si din Lf cea maifrecventa cauza de masa mediast

    Mediastin A si M 70% simptomatici (local/ general)

    LH LMNH

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    GUSA PLONJANTA

    10% din masele mediastinale

    20% M

    Simptome apar si in formele B

    Rx, CT +/- scinti

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    MEDIASTIN ANTEROSUPERIOR

    T timica , HT timica

    Teratom (B, M), seminom

    Limfom

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    TUMORI TIMICE

    B/M

    Mediastin AS

    Cea mai frecventa T mediast primara

    Decada 5-6, B=F, unilat Sdr paraneo

    - miastenia gravis

    - hipoglobulinemie

    - aplazie eritrocitara

    HT timica decade 1-2

    Asociaza miastenia gravis, HTy, ICSR, acromegalie

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    TUMORI GERMINATIVE

    Seminom voluminos, ant, stg, HCG

    Teratom benign fete, voluminos, resturi

    ectodemice

    Teratom malign meta, creste repede

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    MEDIASTIN MIJLOCIU

    Adenopatii - LH, neo bronsic, sin

    - infectii (tbc)

    - sarcoidoza Chist pericardic

    Chist bronhogen

    Anevrism Ao Hernia Morgagni

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    SARCOIDOZA

    B granulomatoasa necazeoasa

    Ap simetrice hilare/ mediastinale

    Asimpt/simpt: astenie, tuse, dispnee,eritem nodos, uveita

    Dg: biopsie cutanata/ ggl

    Evolutie stationara/ remisie/progresiva

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    HERNIA MORGAGNI

    3 M: medial, mature, minuscule

    Femeie, obeza, de virsta medie

    Mal formarea septului transvers

    dr>stg

    +/- defecte pericardice

    Dispnee, tuse, simpt dig sup nespec

    Complicatii: incarcerare

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    MEDIASTIN POSTERIOR

    T neurogene (schwanom, neurofibrom,feocromocitom)

    Anevrism Ao desc Diverticuli E (Zenker, epifrenici, interbronsici)

    Carcinom esofagian

    Hernii (de alunecare, paraesofagiana, Bogdaleck) Hematopoeza extramedulara

    Pseudochist pancreatic

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    ANEVRISM DE AORTA

    Crosa SVCS + pusatii si expansiunesuprasternala

    Crosa si Ao asc comprima laringeulrecurent + osteita sternala

    Ao desc disfagie + nevralgie ic + osteitavertebrala

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    HERNIA HIATALA

    Cea mai frecventa

    Nivel hidroaeric posterior de cord, de

    obicei pe stg.

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    HERNIA BOGDALECK

    - 3B : baby, back (posterolateral), big

    - stg>dr

    - Lipsa de inchidere a faldului pleuroperitoneal

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    SINDROMUL DE VCS

    Dispnee, cefalee, obstructie nazala, tulburare deconstienta, coma

    Edem, cianoza, circulatie colaterala, stridor, edem

    papilar

    Compresie

    Invazie

    Tromboza

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    SINDROMUL DE VCS

    C pulmonar, LH, meta

    Fibroza mediastinala

    Anevrism de Ao

    Histoplasmoza, TBC, lues T benigne

    Tromboza (cateter venos central, pacemaker)

    CT sediul/ mec obstructiei RMN vizualizeaza direct fluxul sangvin

    Venografie circulatia colaterala

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    Venografie - sdr VCS

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    Anatomia VCS si a venelormediastinului

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    SINDROM MEDIASTINAL

    Dispnee

    Durere toracica

    Disfagie Disfonie

    Edem in pelerina

    Cianoza in pelerina

    Circulatie colaterala

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    Timom

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    LIMFOM

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    pneumomediastin

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    HH

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    ti

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    timom

    timom

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    timom

    Rest timic

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    Rest timic

    pneumomediastin

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    pneumomediastin

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    Meta melanom

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    Meta melanom

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    Fibroza de iradiere

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    limfom

    G l j t

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    Gusa plonjanta

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    T neurogena

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    Anevrism de aorta descendenta


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